Achenbach’s syndrome: A case report of the paroxysmal blue finger in a middle-aged woman

Harisankar Anantharajan1, Peter Bjerring1, Luit Penninga2, Theis Mariager3, Carsten Sauer Mikkelsen2,4

1Department of Dermato-Venereology, Aalborg University Hospital, Aalborg, Denmark, 2Department of Surgery and Transplantation, Rigshospitalet, Copenhagen University Hospital, Copenhagen, Denmark, 3Department of Infectious Diseases, Aalborg University Hospital, Aalborg, Denmark., 4Private Practice in Dermato-Venereology, Brønderslev, Denmark

Corresponding author: Harisankar Anantharajan, MD, E-mail: harisankar9931@gmail.com

How to cite this article: Anantharajan H, Bjerring P, Penninga L, Mariager T, Mikkelsen CS. Achenbach’s syndrome: A case report of the paroxysmal blue finger in a middle-aged woman. Our Dermatol Online. 2025;16(3):311-312.
Submission: 25.02.2025; Acceptance: 12.05.2025
DOI: 10.7241/ourd.20253.19

Citation tools: 

Related Content

Copyright information

© Our Dermatology Online 2025. No commercial re-use. See rights and permissions. Published by Our Dermatology Online.


ABSTRACT

Achenbach’s syndrome is a rare, benign vascular condition characterized by spontaneous bruising and discoloration of the digits, predominantly affecting middle-aged women. Herein, we present the case of a 55-year-old female with a ten-year history of recurrent, painful discoloration of the fingers, primarily triggered by physical activity. Clinical examination revealed subcutaneous hematoma with normal capillary refill and no systemic involvement. Comprehensive laboratory investigations, including coagulation studies and autoimmune screening, were unremarkable. The condition resolved spontaneously within 5–7 days without intervention. This case highlights the importance of recognizing Achenbach’s syndrome to avoid unnecessary invasive testing and the patient’s anxiety. The characteristic presentation, self-limiting nature, and benign course distinguish it from other vascular conditions requiring urgent intervention.

Key words: Achenbach’s syndrome, paroxysmal finger hematoma, acute idiopathic blue finger, vascular conditions


INTRODUCTION

Achenbach’s syndrome is a rare, benign vascular condition characterized by spontaneous bruising of the digits [1]. First described by Walter Achenbach in 1958, this condition predominantly affects middle-aged women [2,3]. The recognition of this syndrome is crucial to prevent unnecessary diagnostic procedures and the patient’s anxiety [4].

CASE REPORT

A 55-year-old woman presented with a ten-year history of recurrent painful discoloration of the fingers. Episodes occurred spontaneously or following physical activity, affecting primarily the left thumb (Fig. 1) [5]. Physical examination revealed subcutaneous hematoma with normal capillary refill. Laboratory investigations, including platelet count, coagulation profile, C-reactive protein, and autoantibody screening, were unremarkable [6]. The condition resolved spontaneously within 5–7 days without intervention.

Figure 1: Characteristics of Achenbach’s syndrome: subcutaneous hematoma affecting the patient’s left thumb.

DISCUSSION

This case illustrated the classic presentation of Achenbach’s syndrome [7]. The patient’s age, sex, and clinical presentation aligned with the typical features of this condition [1,3]. The spontaneous resolution without complications and normal laboratory findings supported the benign nature of this syndrome [4].

Achenbach’s syndrome is a benign, self-limiting condition with unknown etiology that predominantly affects middle-aged women, with a female-to-male ratio of approx. 8:1. The condition is characterized by spontaneous bleeding from fragile capillaries or small veins, with 70% of cases occurring spontaneously and 30% following minor trauma or hand activity. Despite its alarming appearance, it has no association with systemic vascular diseases or coagulopathies. The characteristic acute onset and self-limiting nature help to differentiate it from other causes of discoloration, and no specific treatment is required, making it important to avoid unnecessary interventions [2,3].

Its pathophysiology remains unclear, although some theories suggest microtrauma to digital vessels or the role of abnormal vascular fragility. The benign nature of this condition makes it crucial for healthcare providers to recognize its clinical presentation to prevent unnecessary diagnostic procedures and the patient’s anxiety. Understanding these characteristics helps to differentiate it from more serious vascular conditions requiring urgent intervention [5,6].

CONCLUSION

Achenbach’s syndrome remains a diagnosis of exclusion yet should be considered in cases of spontaneous digital bruising, particularly in middle-aged women [7]. This case emphasized the importance of recognizing this benign condition to avoid unnecessary investigations and interventions [1,4].

ACKNOWLEDGMENTS

We thank the patient for providing consent for the publication of this case report.

Consent

The examination of the patient was conducted according to the principles of the Declaration of Helsinki.

The authors certify that they have obtained all appropriate patient consent forms, in which the patients gave their consent for images and other clinical information to be included in the journal. The patients understand that their names and initials will not be published and due effort will be made to conceal their identity, but that anonymity cannot be guaranteed.

REFERENCES

1.Takeuchi H, Uchida HA, Okuyama Y, Wada J. Acute idiopathic blue fingers:A young man with Achenbach’s syndrome. BMJ Case Rep. 2016 Apr 18;2016:10.1136/bcr-2016-214491.

2.Gomes JF, Mendes J, Donaire D, Ferreira M. Achenbach’s syndrome. BMJ Case Rep. 2020;13:238156.

3.Matellanes-Palacios M, Sabater-Abad J. Visual dermatology:Achenbach’s syndrome (paroxismal finger hematoma). J Cutan Med Surg. 2021;25:206.

4.Godoy A, Tabares AH. Achenbach syndrome (paroxysmal finger hematoma). Vasc Med. 2019;24:361-6.

5.Woods M, Iftikhar S. A case of the blue finger:Achenbach syndrome. R I Med J (2013). 2020;103:27-8.

6.Robertson A, et al. Achenbach’s syndrome:A comprehensive review of clinical presentations and management. J Clin Med. 2023;12:2891.

7.Chen K, Liu Y. Paroxysmal finger hematoma:Recognition and clinical significance. Int J Dermatol. 2024;63:45-51.

Notes

Source of Support: This article has no funding source.

Conflict of Interest: The authors have no conflict of interest to declare.

Copyright by authors of this article. This is an open-access article distributed under the terms of the Creative Commons Attribution License, which permits unrestricted use, distribution, and reproduction in any medium, provided the original author and source are credited.

Request permissions
If you wish to reuse any or all of this article please use the e-mail (contact@odermatol.com) to contact with publisher.

Related Content:

Related Articles Search Authors in

http://orcid.org/0009-0000-7957-8363
http://orcid.org/0000-0002-3031-1390
http://orcid.org/0000-0002-8531-1865
http://orcid.org/0000-0001-8135-561X
http://orcid.org/0000-0002-1202-462X

Rights and permissions

This work is licensed under a Creative Commons Attribution-NonCommercial 4.0 International License.

Comments are closed.